ADAM12

ADAM12
Identifikatori
AliasiADAM12
Vanjski ID-jeviOMIM: 602714 MGI: 105378 HomoloGene: 74862 GeneCards: ADAM12
Lokacija gena (čovjek)
Hromosom 10 (čovjek)
Hrom.Hromosom 10 (čovjek)[1]
Hromosom 10 (čovjek)
Genomska lokacija za ADAM12
Genomska lokacija za ADAM12
Bend10q26.2Početak126,012,381 bp[1]
Kraj126,388,477 bp[1]
Lokacija gena (miš)
Hromosom 7 (miš)
Hrom.Hromosom 7 (miš)[2]
Hromosom 7 (miš)
Genomska lokacija za ADAM12
Genomska lokacija za ADAM12
Bend7|7 F3Početak133,484,928 bp[2]
Kraj133,833,875 bp[2]
Obrazac RNK ekspresije




Više referentnih podataka o ekspresiji
Ontologija gena
Molekularna funkcija SH3 domain binding
GO:0070122 peptidase activity
metalloendopeptidase activity
GO:0001948, GO:0016582 vezivanje za proteine
hydrolase activity
vezivanje iona metala
metallopeptidase activity
Ćelijska komponenta integral component of membrane
extracellular region
membrana
nukleoplazma
ćelijska membrana
Biološki proces Ćelijska adhezija
myoblast fusion
Proteoliza
extracellular matrix organization
positive regulation of angiogenesis
Izvori:Amigo / QuickGO
Ortolozi
VrsteČovjekMiš
Entrez
Ensembl
UniProt
RefSeq (mRNK)

NM_021641
NM_001288973
NM_001288974
NM_001288975
NM_003474

NM_007400

RefSeq (bjelančevina)

NP_001275902
NP_001275903
NP_001275904
NP_003465
NP_067673

NP_031426

Lokacija (UCSC)Chr 10: 126.01 – 126.39 MbChr 7: 133.48 – 133.83 Mb
PubMed pretraga[3][4]
Wikipodaci
Pogledaj/uredi – čovjekPogledaj/uredi – miš

Protein 12 koji sadrži domen dezintegrina i metaloproteinaze (ranije Meltrin) je enzim koji je kod ljudi kodiran genom ADAM12.[5][6] ADAM12 ima dvije splajs varijante: ADAM12-L, dugi oblik, ima transmembransku regiju i ADAM12-S, kraća varijanta, je rastvorljiva i nema transmembranski i citoplazmatski domen.[7]

Funkcija

Ovaj gen kodira člana proteinske porodice ADAM (dizintegrin i metaloproteinaza). Članovi ove porodice su proteini usidreni u membrani, strukturno srodni zmijskim otrovima disintegrin, i uključeni su u različite biološke procese koji uključuju interakcije ćelija-ćelija i ćelija-matriks, uključujući oplodnju, razvoj mišića i neurogenezu. Ovaj gen ima dva alternativno spojena transkripta: kraći sekretovani oblik i duži membranski vezan oblik. Utvrđeno je da kraći oblik stimuliše miogenezu.[8]

Klinički značaj

ADAM 12, metaloproteinaza koja veže protein-3 koji veže faktor rasta inzulina (IGFBP-3), čini se da je efikasan rani marker Downovog sindroma. Smanjeni nivoi ADAM 12 mogu se otkriti u slučajevima trisomije 21 već u 8. do 10. sedmici trudnoće. Nivoi ADAM 12 i PAPP-A u majčinom serumu u 8. do 9. sedmici trudnoće u kombinaciji s dobi majke dali su stopu detekcije Downovog sindroma od 91% uz stopu lažno pozitivnih rezultata od 5%. Kada su dodani podaci o njušnoj translucenciji iz približno 12. sedmice trudnoće, ovo je povećalo stopu detekcije na 97%.[9]

ADAM12 je također povezan s razvojem patoloških promjena kod različitih kancera, hipertenzije, jetrene fibrogeneze i astme.[10] Kod astme, ADAM12 je pojačano izražen u plućnom epitelu kao odgovor na TNF-alfa.[11]

U studiji provedenoj na oko 1200 osoba s izuzetno visokom inteligencijom (IQ oko 170), varijante gena bile su povezane s visokim IQ-om u usporedbi s općom populacijom.[12]

Interakcije

Pokazano je da je ADAM12 u interakciji sa:

Reference

  1. ^ a b c GRCh38: Ensembl release 89: ENSG00000148848 - Ensembl, maj 2017
  2. ^ a b c GRCm38: Ensembl release 89: ENSMUSG00000054555 - Ensembl, maj 2017
  3. ^ "Human PubMed Reference:". National Center for Biotechnology Information, U.S. National Library of Medicine.
  4. ^ "Mouse PubMed Reference:". National Center for Biotechnology Information, U.S. National Library of Medicine.
  5. ^ Gilpin BJ, Loechel F, Mattei MG, Engvall E, Albrechtsen R, Wewer UM (Feb 1998). "A novel, secreted form of human ADAM 12 (meltrin alpha) provokes myogenesis in vivo". J. Biol. Chem. 273 (1): 157–66. doi:10.1074/jbc.273.1.157. PMID 9417060.
  6. ^ Kveiborg M, Albrechtsen R, Couchman JR, Wewer UM (Jun 2008). "Cellular roles of ADAM12 in health and disease". Int. J. Biochem. Cell Biol. 40 (9): 1685–702. doi:10.1016/j.biocel.2008.01.025. PMID 18342566.
  7. ^ Yagami-Hiromasa T, Sato T, Kurisaki T, Kamijo K, Nabeshima Y, Fujisawa-Sehara A (1995). "A metalloprotease-disintegrin participating in myoblast fusion". Nature. 377 (6550): 652–6. Bibcode:1995Natur.377..652Y. doi:10.1038/377652a0. PMID 7566181. S2CID 4348744.
  8. ^ "Entrez Gene: ADAM12 ADAM metallopeptidase domain 12 (meltrin alpha)".
  9. ^ Danforth's Obstetrics and Gynecology, 10th Edition; Copyright ©2008 Lippincott Williams & Wilkins; Chapter 7: Prenatal Diagnosis, Page 113
  10. ^ Nyren-Erickson EK, Jones JM, Srivastava DK, Mallik S (2013). "A disintegrin and metalloproteinase-12 (ADAM12): function, roles in disease progression, and clinical implications". Biochim. Biophys. Acta. 1830 (10): 4445–55. doi:10.1016/j.bbagen.2013.05.011. PMC 3740046. PMID 23680494.
  11. ^ Estrella C, Rocks N, Paulissen G, Quesada-Calvo F, Noel A, Vilain E, Lassalle P, Tillie-Leblond I, Cataldo D, Gosset P (2009). "Role of a disintegrin and metalloprotease-12 in neutrophil recruitment induced by airway epithelium". Am. J. Respir. Cell Mol. Biol. 41 (4): 449–58. doi:10.1165/rcmb.2008-0124OC. hdl:2268/5767. PMID 19213876.
  12. ^ Dzirasa, Kafui (2. 8. 2017). "A brilliant approach to study the basis of intelligence?". Science Translational Medicine (jezik: engleski). 9 (401). doi:10.1126/scitranslmed.aao0978. ISSN 1946-6234. S2CID 44125138.
  13. ^ Galliano MF, Huet C, Frygelius J, Polgren A, Wewer UM, Engvall E (maj 2000). "Binding of ADAM12, a marker of skeletal muscle regeneration, to the muscle-specific actin-binding protein, alpha -actinin-2, is required for myoblast fusion". J. Biol. Chem. 275 (18): 13933–9. doi:10.1074/jbc.275.18.13933. PMID 10788519.
  14. ^ Shi Z, Xu W, Loechel F, Wewer UM, Murphy LJ (Jun 2000). "ADAM 12, a disintegrin metalloprotease, interacts with insulin-like growth factor-binding protein-3". J. Biol. Chem. 275 (24): 18574–80. doi:10.1074/jbc.M002172200. PMID 10849447.
  15. ^ Loechel F, Fox JW, Murphy G, Albrechtsen R, Wewer UM (Nov 2000). "ADAM 12-S cleaves IGFBP-3 and IGFBP-5 and is inhibited by TIMP-3". Biochem. Biophys. Res. Commun. 278 (3): 511–5. Bibcode:2000BBRC..278..511L. doi:10.1006/bbrc.2000.3835. PMID 11095942.
  16. ^ Kang Q, Cao Y, Zolkiewska A (Jul 2001). "Direct interaction between the cytoplasmic tail of ADAM 12 and the Src homology 3 domain of p85alpha activates phosphatidylinositol 3-kinase in C2C12 cells". J. Biol. Chem. 276 (27): 24466–72. doi:10.1074/jbc.M101162200. PMID 11313349.

Dodatno štivo

Vanjski linkovi

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