ASRGL1

ASRGL1
Dostupne strukture
PDBPretraga ortologa: PDBe RCSB
Spisak PDB ID kodova

3TKJ, 4ET0, 4O0C, 4O0D, 4O0E, 4O0F, 4O0G, 4O0H, 4OSX, 4OSY, 4PVP, 4PVQ, 4PVR, 4PVS, 4ZM9

Identifikatori
AliasiASRGL1
Vanjski ID-jeviOMIM: 609212 MGI: 1913764 HomoloGene: 11825 GeneCards: ASRGL1
EC broj3.5.1.1 3.4.19.5, 3.5.1.1
Lokacija gena (čovjek)
Hromosom 11 (čovjek)
Hrom.Hromosom 11 (čovjek)[1]
Hromosom 11 (čovjek)
Genomska lokacija za ASRGL1
Genomska lokacija za ASRGL1
Bend11q12.3Početak62,337,448 bp[1]
Kraj62,393,412 bp[1]
Lokacija gena (miš)
Hromosom 19 (miš)
Hrom.Hromosom 19 (miš)[2]
Hromosom 19 (miš)
Genomska lokacija za ASRGL1
Genomska lokacija za ASRGL1
Bend19|19 APočetak9,087,232 bp[2]
Kraj9,113,000 bp[2]
Obrazac RNK ekspresije
Više referentnih podataka o ekspresiji
Ontologija gena
Molekularna funkcija GO:0070122 peptidase activity
beta-aspartyl-peptidase activity
hydrolase activity
N4-(beta-N-acetylglucosaminyl)-L-asparaginase activity
asparaginase activity
Ćelijska komponenta citoplazma
citosol
jedro
photoreceptor inner segment
Biološki proces asparagine catabolic process via L-aspartate
L-phenylalanine catabolic process
Proteoliza
protein maturation
Izvori:Amigo / QuickGO
Ortolozi
VrsteČovjekMiš
Entrez
Ensembl
UniProt
RefSeq (mRNK)

NM_001083926
NM_025080

NM_025610

RefSeq (bjelančevina)

NP_001077395
NP_079356

NP_079886

Lokacija (UCSC)Chr 11: 62.34 – 62.39 MbChr 19: 9.09 – 9.11 Mb
PubMed pretraga[3][4]
Wikipodaci
Pogledaj/uredi – čovjekPogledaj/uredi – miš

L-asparaginaza je enzim koji je kod ljudi kodiran genom ASRGL1.[5]

Aminokiselinska sekvenca

Dužina polipeptidnog lanca je 308 aminokiselina, a molekulska težina 32.055 Da.[6].

1020304050
MNPIVVVHGGGAGPISKDRKERVHQGMVRAATVGYGILREGGSAVDAVEG
AVVALEDDPEFNAGCGSVLNTNGEVEMDASIMDGKDLSAGAVSAVQCIAN
PIKLARLVMEKTPHCFLTDQGAAQFAAAMGVPEIPGEKLVTERNKKRLEK
EKHEKGAQKTDCQKNLGTVGAVALDCKGNVAYATSTGGIVNKMVGRVGDS
PCLGAGGYADNDIGAVSTTGHGESILKVNLARLTLFHIEQGKTVEEAADL
SLGYMKSRVKGLGGLIVVSKTGDWVAKWTSTSMPWAAAKDGKLHFGIDPD
DTTITDLP

Funkcija

Protein ASRGL1 sastoji se od 308 aminokiselina i aktivira se automatskim cijepanjem na aminokiselini 168, kako bi formirao alfa- i beta-lanac, koji se može dimerizirati u heterodimer.[7] Enzim ASRGL1 ima aktivnost i L-asparaginaze i beta-aspartil peptidaze i može biti uključen u proizvodnju L-aspartata, koji može djelovati kao ekscitacijski neurotransmiter u nekim regijama mozga.

Prema analizi profila i transkriptomike zasnovanoj na antitijelima, protein ASRGL1 prisutan je u svim analiziranim ljudskim tkivima, s najvećom ekspresijom u mozgu, u ženskim tkivima kao što su grlić materice i jajovod i muškom tkivu kao u sjemenicima.[8] Na osnovu konfokusne mikroskopije, ASRGL1 je uglavnom lokaliziran na mikrotubulama.[9]

Klinički značaj

ASRGL1 je visoko eksprimiran u normalnom endometriju i različito izražen u karcinomu endometrija. Gubitak ekspresije ASRGL1 nepovoljna je prognostička značajka za pacijente s karcinomom endometrija.[10][11]

Reference

  1. ^ a b c GRCh38: Ensembl release 89: ENSG00000162174 - Ensembl, maj 2017
  2. ^ a b c GRCm38: Ensembl release 89: ENSMUSG00000024654 - Ensembl, maj 2017
  3. ^ "Human PubMed Reference:". National Center for Biotechnology Information, U.S. National Library of Medicine.
  4. ^ "Mouse PubMed Reference:". National Center for Biotechnology Information, U.S. National Library of Medicine.
  5. ^ "Entrez Gene: ASRGL1 asparaginase like 1".
  6. ^ "UniProt, Q7L266". Pristupljeno 16. 8. 2021.
  7. ^ Li, Wenzong; Cantor, Jason R.; Yogesha, S. D.; Yang, Shirley; Chantranupong, Lynne; Liu, June Qingxia; Agnello, Giulia; Georgiou, George; Stone, Everett M. (16. 11. 2012). "Uncoupling Intramolecular Processing and Substrate Hydrolysis in the N-Terminal Nucleophile Hydrolase hASRGL1 by Circular Permutation". ACS Chemical Biology. 7 (11): 1840–1847. doi:10.1021/cb300232n. ISSN 1554-8929. PMC 3514461. PMID 22891768.
  8. ^ "Tissue expression of ASRGL1 - Summary - The Human Protein Atlas". www.proteinatlas.org. Pristupljeno 3. 10. 2017.
  9. ^ "Cell atlas - ASRGL1 - The Human Protein Atlas". www.proteinatlas.org. Arhivirano s originala, 3. 1. 2019. Pristupljeno 3. 10. 2017.
  10. ^ "Expression of ASRGL1 in endometrial cancer - The Human Protein Atlas". www.proteinatlas.org. Pristupljeno 3. 10. 2017.
  11. ^ Edqvist, Per-Henrik D.; Huvila, Jutta; Forsström, Björn; Talve, Lauri; Carpén, Olli; Salvesen, Helga B.; Krakstad, Camilla; Grénman, Seija; Johannesson, Henrik (2015). "Loss of ASRGL1 expression is an independent biomarker for disease-specific survival in endometrioid endometrial carcinoma". Gynecologic Oncology. 137 (3): 529–537. doi:10.1016/j.ygyno.2015.03.055. PMID 25858696.

Dopunska literatura

Vanjski linkovi

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